RT Journal Article SR Electronic T1 Ameloblastic Fibrosarcoma Arising in the Maxilla JF Ochsner Journal JO Ochsner J FD O. P. Jindal Global University SP 143 OP 145 VO 16 IS 2 A1 Rachael R. Pillay A1 Arthur Bilski A1 Martin Batstone YR 2016 UL http://www.ochsnerjournal.org/content/16/2/143.abstract AB Background: Ameloblastic fibrosarcoma (AFS) is a rare odontogenic neoplasm of the jaw that usually arises de novo or through a malignant change in the mesenchymal component of a preexisting or recurrent benign fibroma. The majority of AFS cases reported in the literature arise in the mandible.Case Report: A 35-year-old male presented with an asymptomatic left maxillary mass that on imaging was found to be effacing most of his maxillary sinus. He underwent a left maxillectomy with free-flap reconstruction and adjuvant radiotherapy to the tumor bed.Conclusion: Wide local excision remains the treatment of choice for AFS, given the poor survival rates of patients with recurrent disease. However, long-term studies and follow-up are needed to elucidate the role of adjuvant therapies in the primary treatment of AFS.