TY - JOUR T1 - Pulmonary Hypertension in a Patient With Congenital Heart Defects and Heterotaxy Syndrome JF - Ochsner Journal JO - Ochsner J SP - 309 LP - 311 VL - 16 IS - 3 AU - Tariq Yousuf AU - Jason Kramer AU - Brody Jones AU - Hesam Keshmiri AU - Muhyaldeen Dia Y1 - 2016/09/21 UR - http://www.ochsnerjournal.org/content/16/3/309.abstract N2 - Background: Heterotaxy syndrome, also called isomerism, is a condition in which abdominal and thoracic organs are located in abnormal body positions. Pulmonary hypertension (PHTN) is an uncommon clinical feature of heterotaxy syndrome.Case Report: We describe the case of a 26-year-old male who developed PHTN as a rare manifestation of heterotaxy syndrome. To our knowledge, PHTN has never been reported as a prominent clinical feature in a patient with heterotaxy syndome and congenital cardiac abnormalities.Conclusion: It is important for the clinician to be aware of potentially serious consequences of PHTN in the setting of heterotaxy syndrome. ER -