Original ArticleVascular Anomalies Associated with Esophageal Atresia and Tracheoesophageal Fistula
Section snippets
Methods
This study was a retrospective review of all patients born with EA/TEF between January 2005 and October 2013 and followed at Sainte Justine Hospital. The study was approved by the local Institutional Review Board.
Patients were excluded from the analysis if they had been operated on elsewhere or if death occurred in the first week of life. Data were collected using standardized data abstraction forms. The abstracted information included the following patient-level variables: sex, birth weight,
Results
A total of 86 patients with EA/TEF born between January 2005 and October 2013 were seen at Sainte Justine Hospital. Ten children had insufficient data or follow-up, including 3 children who died in the first week of life and 7 children who underwent surgery elsewhere (Figure 2; available at www.jpeds.com.)
Seventy-six patients (36 females; 47%) met the inclusion criteria. The median birth weight was 2530 g (range, 1065-4400 g), and median gestational age was 37 weeks (range, 29-41 weeks). Seven
Discussion
We report that the overall incidence of ARSA and RAA is 18% in children who undergo surgery for EA/TEF. Long-gap EA and severe cardiac malformations requiring surgery are both significantly associated with vascular anomalies. We also show that the clinical consequences are variable, ranging from no symptoms to severe respiratory problems and dysphagia. The diagnostic yield of routinely used techniques–preoperative cardiac ultrasound and esophagram–is not optimal.
Congenital vascular anomalies
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2021, Advances in PediatricsCitation Excerpt :Five percent of patients with EA have a right-sided arch, which may complicate exposure during the repair [19]. In addition, patients with EA can have other vascular anomalies, including double aortic arch, circumflex aorta, and/or aberrant right subclavian arteries, which, if suspected, can be further evaluated with a computed tomography angiogram or cardiac MRI [8,20,21]. Other commonly associated anomalies include those of the musculoskeletal system, genitourinary tract, intestine, spine, and craniofacial locations (see Table 1).
Aberrant Right Subclavian Artery to Esophageal Fistula: A Rare Case and Its Management
2020, Annals of Thoracic Surgery
The authors declare no conflicts of interest.