Surgical correction of mitral valve prolapse : a cure for recurrent ventricular tachycardia in Marfan syndrome?

Rebecca S Beroukhim; John H Reed; Michael S Schaffer; Anji T Yetman

doi:10.1007/s00246-006-1102-0

Surgical correction of mitral valve prolapse : a cure for recurrent ventricular tachycardia in Marfan syndrome?

Pediatr Cardiol. 2006 Nov-Dec;27(6):755-8. doi: 10.1007/s00246-006-1102-0. Epub 2006 Sep 30.

Authors

Rebecca S Beroukhim¹, John H Reed, Michael S Schaffer, Anji T Yetman

Affiliation

¹ Children's Hospital Heart Institute, University of Colorado Health Sciences Center & The Children's Hospital, 1056 E. 19th Avenue, B-100, Denver, CO 80218, USA.

PMID: 17019535
DOI: 10.1007/s00246-006-1102-0

Abstract

We describe the case of a 3-year-old child with neonatal Marfan syndrome complicated by mitral valve prolapse with regurgitation, marked aortic root dilatation, and ventricular tachycardia. The patient had resolution of ventricular tachycardia following surgical intervention consisting of a valve-sparing aortic root replacement and mitral valve annuloplasty.

Publication types

Case Reports

MeSH terms

Amiodarone / therapeutic use
Anti-Arrhythmia Agents / therapeutic use
Child, Preschool
Electrocardiography
Electrocardiography, Ambulatory
Humans
Male
Marfan Syndrome / complications*
Mitral Valve Prolapse / complications*
Mitral Valve Prolapse / surgery*
Recurrence
Tachycardia, Ventricular / etiology
Tachycardia, Ventricular / surgery*

Substances

Anti-Arrhythmia Agents
Amiodarone