Elsevier

The Lancet

Volume 336, Issue 8721, 20 October 1990, Pages 965-967
The Lancet

Antenatal intervention for congenital cystic adenomatoid malformation

https://doi.org/10.1016/0140-6736(90)92420-MGet rights and content

Abstract

In 2 fetuses with congenital cystic adenomatoid malformation (CCAM) with hydrops, in-utero resection of the enlarged pulmonary lobe reduced mediastinal shift and allowed expansion of normal lung tissue in both cases. In case 1, the 27-week-gestation fetus died from severe hydrops after premature delivery. In case 2, fetal CCAM resection was completed at 23 weeks' gestation. At 30 weeks a girl was delivered with no evidence of pulmonary hypoplasia. Fetal surgery can now be entertained for otherwise fatal space-occupying intrathoracic lesions.

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